WebSpecialty. Endocrinology. Danon disease (or glycogen storage disease Type IIb) is a metabolic disorder. [1] Danon disease is an X-linked lysosomal and glycogen storage disorder associated with hypertrophic cardiomyopathy, skeletal muscle weakness, and intellectual disability. [2] It is inherited in an X-linked dominant pattern. WebImpact. As part of Danone Renew strategy, the company reframed its sustainability journey, articulated around 3 pillars: Health, Nature and People & Communities . For each pillar, Danone defines a new set of priorities which are translated into mid to long-term objectives, focusing on where the company can deliver the most impact and value.

Dan On Foods Corporation

WebAs part of its commitment, Dannon pledged to reduce the amount of total sugar to 23 … WebDéjà de nouvelles réductions alléchantes ! Vous retrouverez régulièrement des bons de réduction pour toute la famille sur les différentes marques Danone, valables en magasin, en vous connectant à votre compte ou en … can i shock treat thru my water softener

Danon Disease - GeneReviews® - NCBI Bookshelf

WebSep 30, 2024 · Danon Disease is a rare X-linked inherited disorder caused by mutations in the gene encoding lysosome-associated membrane protein 2 (LAMP-2), an important mediator of autophagy. This results in accumulation of autophagosomes and glycogen, particularly in cardiac muscle and other tissues, which ultimately leads to heart failure, … WebJul 9, 2024 · THE DANNON COMPANY MEETS AND IN SOME CASES EXCEEDS ITS … WebClinical trials are in process that use gene therapy to fight Danon disease. In a phase 1 trial conducted at Children's Hospital of Philadelphia (CHOP), six patients (four adults and two children) received a one-time intravenous infusion of RP-A501. RP-A501 is an experimental adeno-associated virus (AAV)-based gene therapy, which replaces the ... five letter word with letters o u r